Improvement of Dilated Cardiomyopathy with Methylprednisolone in a Patient with Multiple Fibrosclerosis

authors:

avatar Ibrahim Altun 1 , * , avatar Goksel Guz 2 , avatar Fatih Akin 1 , avatar Nuri Kose 1 , avatar Ilknur Altun 3 , avatar Zeki Yuksel Gunaydin 4 , avatar Cem Sahin 5

Mugla Sitki Kocman University, Faculty of Medicine, Department of Cardiology, Mugla, Turkey
Istanbul University, Faculty of Medicine, Department of Cardiology, Istanbul, Turkey
Mugla Sitki Kocman University, Faculty of Medicine, Department of Radiology, Mugla, Turkey
Istanbul University, Faculty of Medicine, Department of Cardiology, Istanbul,, Turkey
Mugla Sitki Kocman University, Faculty of Medicine, Department of Internal Medicine, Mugla, Turkey
International Cardiovascular Research Journal: Vol.8, issue 4; e11683
published online: December 01, 2014
article type: Case Report
received: April 19, 2017
accepted: July 28, 2014

how to cite: Altun I , Guz G , Akin F, Kose N , Altun I , et al. Improvement of Dilated Cardiomyopathy with Methylprednisolone in a Patient with Multiple Fibrosclerosis. Int Cardiovasc Res J. 2014;8(4):e11683. 

Abstract

Multifocal fibrosclerosis is a rare syndrome of unknown cause that is characterized by fibrosis involving multiple organ systems. Definitive diagnosis can only be made based on biopsy findings. In this case, the biopsy specimen of the patient demonstrates pulmonary hyalinated granuloma or sclerosing mediastinitis. There are few reports of multiple fibrosclerosis with heart failure. Here, we reported a case of retroperitoneal fibrosis with massive mediastinal involvement extending to pleura and pericardium causing pleuro- pericardial effusion with dilated cardiomyopathy. Systolic dysfunction was improved and pericardial effusion disappeared with methylprednisolone treatment.

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References

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